ICD-11 classes
16 Diseases of the genitourinary system
Diseases of the female genital system
Dermatoses of female genitalia
GA40 — Inflammatory dermatoses of the vulva
EB60.0 — Lichen sclerosus of vulva

ICD-11 EB60.0 — Lichen sclerosus of vulva

Lichen sclerosus of the vulva is an inflammatory disorder of unknown aetiology affecting the skin of the vulva and perianal area. Typically it affects women in the fifth and sixth decades of life though is not uncommon in prepubertal girls. It presents with pruritus, soreness or dyspareunia. The affected skin is white and atrophic, though secondary changes including maceration, purpura and erosion may dominate the clinical picture. In longstanding cases there may be marked shrinkage of the vulva, labial fusion and an increased risk of malignant transformation.

The diagnosis includes nothing.

The diagnosis excludes nothing.

It has no clarifying diagnoses.

The diagnosis is coded elsewhere:

• Lichen sclerosus #15815
• Inflammatory dermatoses of the vulva #16943