ICD-11 classes
16 Diseases of the genitourinary system
Diseases of the urinary system
Glomerular diseases
Clinical findings in specimens from the urinary system
MF81 — Fibronectin glomerulopathy
ICD-11 MF81 — Fibronectin glomerulopathy
Fibronectin glomerulopathy is a rare hereditary kidney disease in which fibronectin (FN1) deposits are seen in the mesangium and subendothelial space. The clinical picture is characterised by proteinuria, type IV renal tubular acidosis, microscopic haematuria and hypertension that may lead to end-stage renal failure in the second to sixth decade of life. This disease may be associated with mutations in the FN1 gene.
The diagnosis includes nothing.
The diagnosis excludes nothing.
It has no clarifying diagnoses.
The diagnosis is coded elsewhere: