ICD-11 classes
16 Diseases of the genitourinary system
Diseases of the urinary system
Cystic or dysplastic kidney disease
GB81 — Autosomal dominant polycystic kidney disease
ICD-11 GB81 — Autosomal dominant polycystic kidney disease
Multiple cysts in both kidneys increasing in number and size from adolescence, associated with development of hypertension and chronic renal failure. Autosomal dominant familial pattern is usual and due to mutations on Chromosomes 16 and 4. Non-renal manifestations can include cysts in the liver and less commonly pancreas,. Cerebral arterial aneurysms with subarachnoid haemorrhage, and other non-renal vascular abnormalities can also occur.
The diagnosis includes nothing.
The diagnosis excludes nothing.
It has no clarifying diagnoses.
The diagnosis is coded elsewhere: