ICD-11 classes
19 Certain conditions originating in the perinatal period
Disorders involving the integument of fetus or newborn
KC40 — Miscellaneous skin disorders in the neonate
KA88 — Disseminated intravascular coagulation of fetus or newborn
ICD-11 KA88 — Disseminated intravascular coagulation of fetus or newborn
Neonatal purpura fulminans is a potentially lethal disorder characterised by progressive haemorrhagic necrosis of the skin associated with cutaneous vascular thrombosis. It is usually due to a genetically transmitted thrombophilic disorder: most commonly homozygous deficiency of protein C or, less frequently, protein S.
The diagnosis includes nothing.
The diagnosis excludes nothing.
It has no clarifying diagnoses.
The diagnosis is coded elsewhere: