ICD-11 classes
20 Developmental anomalies
Structural developmental anomalies primarily affecting one...
Structural developmental anomalies of the circulatory system
Structural developmental anomaly of heart or great vessels
LA88 — Congenital anomaly of a ventricle or the ventricular septum
LA88.2 — Tetralogy of Fallot

ICD-11 LA88.2 — Tetralogy of Fallot

A group of congenital cardiovascular malformations with biventricular atrioventricular alignments or connections characterised by anterosuperior deviation of the conal or outlet septum or its fibrous remnant, narrowing or atresia of the pulmonary outflow, a ventricular septal defect of the malalignment type, and biventricular origin of the aorta.Additional information: tetralogy of Fallot will always have a ventricular septal defect, narrowing or atresia of the pulmonary outflow, aortic override, and most often right ventricular hypertrophy.

The diagnosis includes nothing.

The diagnosis excludes nothing.

Diagnosis with code LA88.2 contains 5 clarifying diagnoses:

1. LA88.20 — Tetralogy of Fallot with absent pulmonary valve syndrome
2. LA88.21 — Tetralogy of Fallot with pulmonary atresia
3. LA88.22 — Tetralogy of Fallot with pulmonary atresia and systemic-to-pulmonary collateral artery
4. LA88.2Y — Other specified tetralogy of Fallot
5. LA88.2Z — Tetralogy of Fallot, unspecified

The diagnosis is coded elsewhere:

• Congenital anomaly of a ventricle or the ventricular septum #12054
• Tetralogy of Fallot #12057