ICD-11 classes
20 Developmental anomalies
Structural developmental anomalies primarily affecting one...
Structural developmental anomalies of the liver, biliary...
LB20 — Structural developmental anomalies of gallbladder, bile...
LB20.0 — Structural developmental anomalies of liver
LB20.21 — Biliary atresia
ICD-11 LB20.21 — Biliary atresia
Biliary atresia is a rare disease characterised by an inflammatory biliary obstruction of unknown origin that presents in the neonatal period. It is the most frequent surgical cause of cholestatic jaundice in this age group. Untreated, this condition leads to cirrhosis and death within the first years of life.
The diagnosis includes nothing.
The diagnosis excludes nothing.
It has no clarifying diagnoses.
The diagnosis is coded elsewhere: