ICD-11 classes
20 Developmental anomalies
Multiple developmental anomalies or syndromes
LD20 — Syndromes with central nervous system anomalies as a major...
LD20.3 — Syndromes with holoprosencephaly as a major feature

ICD-11 LD20.3 — Syndromes with holoprosencephaly as a major feature

Any syndrome caused by failure of the prosencephalon to divide in two during the antenatal period. These syndromes may present with closely spaced eyes, cyclopia, flat nasal bridge, single maxillary central incisor, small head size, and clefts of the lip and palate.

The diagnosis includes nothing.

The diagnosis excludes nothing.

Diagnosis with code LD20.3 contains 1 clarifying diagnosis:

1. LA05.4 — Arrhinencephaly

The diagnosis is coded elsewhere:

• Syndromes with central nervous system anomalies as a major feature #8737