ICD-11 classes
20 Developmental anomalies
Multiple developmental anomalies or syndromes
LD24 — Syndromes with skeletal anomalies as a major feature
FB31.1 — Fibrodysplasia ossificans progressiva

ICD-11 FB31.1 — Fibrodysplasia ossificans progressiva

This is an extremely rare disease of the connective tissue where a mutation of the body's repair mechanism causes fibrous tissue (including muscle, tendon, and ligament) to be ossified when damaged.

The diagnosis includes nothing.

The diagnosis excludes nothing.

It has no clarifying diagnoses.

The diagnosis is coded elsewhere:

• Calcification or ossification of muscle #17882
• Progressive ossification of skin, skeletal muscle, fascia, tendons or ligaments #18784
• Syndromes with skeletal anomalies as a major feature #18735
• Progressive ossification of skin, skeletal muscle, fascia, tendons or ligaments #23275