ICD-11 classes
20 Developmental anomalies
Multiple developmental anomalies or syndromes
LD26 — Syndromes with limb anomalies as a major feature
LD26.4 — Arthrogryposis syndromes
LD26.41 — Arthrogryposis multiplex congenita

ICD-11 LD26.41 — Arthrogryposis multiplex congenita

Arthrogryposis multiplex congenita, comprises nonprogressive congenital conditions characterised by multiple joint contractures. The term is currently used in connection with a very heterogeneous group of disorders that all include multiple congenital joint contractures. The major cause of arthrogryposis is fetal akinesia due to fetal abnormalities (e.g. neurogenic, muscle, or connective tissue abnormalities; mechanical limitations to movement) or maternal disorders (e.g. infection, drugs, trauma, other maternal illnesses). generalised fetal akinesia can also lead to polyhydramnios, pulmonary hypoplasia, micrognathia, ocular hypertelorism, and short umbilical cord. Lack of fetal movement causes extra connective tissue to develop around the joint, limiting movement and further aggravating the joint contracture.

The diagnosis includes nothing.

It has no clarifying diagnoses.