ICD-11 classes
20 Developmental anomalies
Multiple developmental anomalies or syndromes
LD27 — Syndromes with skin or mucosal anomalies as a major feature
LD27.0 — Ectodermal dysplasia syndromes
LD27.01 — Cronkhite-Canada syndrome

ICD-11 LD27.01 — Cronkhite-Canada syndrome

Cronkhite-Canada syndrome (CCS) is a sporadically occurring, noninherited disorder of generalised gastrointestinal polyps (hamartomas), cutaneous pigmentation, alopecia, and onychodystrophy. The possibility of progression to cancer is considered to be low. Chronic diarrhea and protein-losing enteropathy are often observed.

The diagnosis includes nothing.

The diagnosis excludes nothing.

It has no clarifying diagnoses.

The diagnosis is coded elsewhere:

• Polyposis syndrome #2669
• Polyposis syndrome #14141
• Polyposis syndrome #14174
• Ectodermal dysplasia syndromes #15941