ICD-11 classes
20 Developmental anomalies
Multiple developmental anomalies or syndromes
LD27 — Syndromes with skin or mucosal anomalies as a major feature
LD27.0 — Ectodermal dysplasia syndromes
LD27.03 — Hidrotic ectodermal dysplasia, Clouston type
ICD-11 LD27.03 — Hidrotic ectodermal dysplasia, Clouston type
Clouston syndrome (or hidrotic ectodermal dysplasia) is an inherited disorder characterised by the clinical triad of nail dystrophy, alopecia, and palmoplantar hyperkeratosis.
The diagnosis includes nothing.
The diagnosis excludes nothing.
It has no clarifying diagnoses.
The diagnosis is coded elsewhere:
- Ectodermal dysplasia syndromes #15941
- Diffuse palmoplantar keratodermas #15961
- Genetic syndromes with alopecia or hypotrichosis #15975
- Genetic syndromes affecting nails #15983
- Diffuse palmoplantar keratodermas #16235
- Genetic syndromes with alopecia or hypotrichosis #16341
- Genetic syndromes affecting nails #16460
- Genetic syndromes affecting nails #23337