ICD-11 classes
20 Developmental anomalies
Multiple developmental anomalies or syndromes
LD27 — Syndromes with skin or mucosal anomalies as a major feature
EC20.0 — Non-syndromic ichthyosis
EC20.03 — Keratinopathic ichthyoses

ICD-11 EC20.03 — Keratinopathic ichthyoses

Heritable ichthyoses resulting from mutations in keratin genes.

The diagnosis includes nothing.

The diagnosis excludes nothing.

It has no clarifying diagnoses.

The diagnosis is coded elsewhere:

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