ICD-11 classes
20 Developmental anomalies
Multiple developmental anomalies or syndromes
LD2A — Malformative disorders of sex development
LD2A.4 — 46,XY disorder of sex development due to androgen resistance

ICD-11 LD2A.4 — 46,XY disorder of sex development due to androgen resistance

Androgen insensitivity syndrome (AIS) is a disorder of sex development (DSD) characterised by the presence of female external genitalia, ambiguous genitalia or variable defects in virilization in a 46,XY individual with absent or partial responsiveness to age-appropriate levels of androgens. It comprises two clinical subgroups: complete AIS (CAIS) and partial AIS (PAIS).

The diagnosis includes nothing.

The diagnosis excludes nothing.

It has no clarifying diagnoses.

The diagnosis is coded elsewhere:

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