ICD-11 classes
20 Developmental anomalies
Multiple developmental anomalies or syndromes
LD2H — Syndromic genetic deafness
LD2H.4 — Usher syndrome
ICD-11 LD2H.4 — Usher syndrome
Usher syndrome is the most common cause of hereditary combined deafness-blindness, and is characterised by the association of sensorineural deafness (usually congenital) with retinitis pigmentosa and progressive vision loss.
The diagnosis includes nothing.
The diagnosis excludes nothing.
It has no clarifying diagnoses.
The diagnosis is coded elsewhere: