ICD-11 classes
20 Developmental anomalies
LD90 — Conditions with disorders of intellectual development as a...
LD90.1 — Early-onset parkinsonism - intellectual deficit

ICD-11 LD90.1 — Early-onset parkinsonism - intellectual deficit

Early-onset parkinsonism with intellectual deficit is a basal ganglia disorder characterised by parkinsonian-type symptoms (postural changes, tremor, rigidity), megalencephaly and variable intellectual deficit. Other signs are frontal bossing, persistent frontal lobe reflexes, strabismus and seizures.

The diagnosis includes nothing.

The diagnosis excludes nothing.

It has no clarifying diagnoses.

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