ICD-11 classes
20 Developmental anomalies
LD90 — Conditions with disorders of intellectual development as a...
8A44.0 — Pelizaeus-Merzbacher disease
LD90.2 — Pelizaeus-Merzbacher-like disease

ICD-11 LD90.2 — Pelizaeus-Merzbacher-like disease

Pelizaeus-Merzbacher like disease (PMLD) is an autosomal recessive leukodystrophy sharing identical clinical and radiological features as X-linked Pelizaeus-Merzbacher disease (PMD; ).

The diagnosis includes nothing.

The diagnosis excludes nothing.

It has no clarifying diagnoses.

The diagnosis is coded elsewhere:

• Pelizaeus-Merzbacher disease #6817
• Conditions with disorders of intellectual development as a relevant clinical feature #23735