ICD-11 classes
02 Neoplasms
Malignant neoplasms, except primary neoplasms of lymphoid,...
Malignant neoplasms, stated or presumed to be primary, of...
Malignant neoplasms of endocrine glands
2D11 — Malignant neoplasms of adrenal gland
ICD-11 2D11 — Malignant neoplasms of adrenal gland
Tumours arising from the adrenal cortex include adenomas and carcinomas. These are rare neoplasms but may cause a variety of hormonal symptoms, including hyperaldosteronism, Cushing syndrome, and virilisation. A small fraction of adrenocortical tumours are associated with an inherited tumour syndrome, including Li-Fraumeni syndrome and Carney complex.Benign and malignant phaeochromocytomas arise in the adrenal medulla and are derived from chromaffin cells of neural crest origin. Phaeochromocytomas may occur in the setting of several hereditary conditions, including multiple endocrine neoplasia types 2a and 2b, von Hippel Lindau disease and neurofibromatosis.Extra adrenal paragangliomas arise from chromaffin cells in sympathoadrenal and parasympathetic paraganglia. They occur in many parts of the body and can pose a significant challenge to surgeons and oncologists. Some function as chemoreceptors, others are endocrinologically active. Familial paragangliomas are associated with mutations of the mitochondrial complex II genes.
The diagnosis includes nothing.
It excludes 1 item.
- Malignant mesenchymal neoplasms (2B50-2B5Z)
Diagnosis with code 2D11 contains 5 clarifying diagnoses:
- 2D11.0 — Adenocarcinoma of adrenal gland
- 2D11.1 — Malignant phaeochromocytoma of adrenal gland
- 2D11.2 — Neuroblastoma of adrenal gland
- 2D11.Y — Other specified malignant neoplasms of adrenal gland
- 2D11.Z — Malignant neoplasms of adrenal gland, unspecified
The diagnosis is coded elsewhere: