ICD-11 classes
02 Neoplasms
In situ neoplasms, except of lymphoid, haematopoietic,...
2E64 — Carcinoma in situ of skin
2E64.1 — Extramammary Paget disease of skin

ICD-11 2E64.1 — Extramammary Paget disease of skin

An intraepithelial adenocarcinoma of apocrine gland-bearing skin and mucous membrane. Clinically it presents as sharply demarcated erythematous plaques most commonly affecting the vulva in women and perianal skin in men.

The diagnosis includes nothing.

The diagnosis excludes nothing.

Diagnosis with code 2E64.1 contains 1 clarifying diagnosis:

  1. 2E67.11 — Vulvar Paget disease

The diagnosis is coded elsewhere:

The diagnosis is included in 1 another class.

  • Vulvar Paget disease (2E67.11)

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