ICD-11 classes
02 Neoplasms
In situ neoplasms, except of lymphoid, haematopoietic,...
2E65 — Carcinoma in situ of breast
2E65.5 — Paget disease of nipple

ICD-11 2E65.5 — Paget disease of nipple

Paget disease of the nipple describes a rare presentation of breast cancer, seen most frequently in women aged 50-60, manifesting with nipple drainage and itching, erythema, crusty, excoriated nipple, thickened plaques and hyperpigmentation (less frequently). It is due to tumour cells invading the nipple-areola complex and represents 1%-3% of all new breast cancer diagnoses.

The diagnosis includes nothing.

The diagnosis excludes nothing.

It has no clarifying diagnoses.

The diagnosis is coded elsewhere:

• Carcinoma in situ of breast #19529