ICD-11 classes
02 Neoplasms
Inherited cancer-predisposing syndromes
LD2D.4 — Gorlin syndrome
ICD-11 LD2D.4 — Gorlin syndrome
Gorlin syndrome, also known as naevoid basal cell carcinoma syndrome (NBCCS), is a hereditary condition characterised by a wide range of developmental abnormalities (odontogenic keratocysts of the jaws, hyperkeratosis of palms and soles, skeletal abnormalities, intracranial ectopic calcifications, and facial dysmorphism) and a predisposition to neoplasms (multiple basal cell carcinomas, medulloblastoma).
It includes 1 item.
- Naevoid basal cell carcinoma syndrome
The diagnosis excludes nothing.
It has no clarifying diagnoses.
The diagnosis is coded elsewhere: