ICD-11 classes
03 Diseases of the blood or blood-forming organs
Anaemias or other erythrocyte disorders
Haemolytic anaemias
Congenital haemolytic anaemia
3A10 — Hereditary haemolytic anaemia
3A10.0 — Haemolytic anaemias due to hexose monophosphate shunt or...
ICD-11 3A10.0 — Haemolytic anaemias due to hexose monophosphate shunt or glutathione metabolism anomalies
This is a form of anaemia due to haemolysis, the abnormal breakdown of red blood cells (RBCs), either in the blood vessels (intravascular haemolysis) or elsewhere in the human body (extravascular). This diagnosis is due to is a process that generates NADPH and pentoses (5-carbon sugars) and glutathione metabolism anomalies.
The diagnosis includes nothing.
The diagnosis excludes nothing.
Diagnosis with code 3A10.0 contains 3 clarifying diagnoses:
- 3A10.00 — Haemolytic anaemia due to glucose-6-phosphate dehydrogenase deficiency
- 3A10.0Y — Other specified haemolytic anaemias due to hexose monophosphate shunt or glutathione metabolism anomalies
- 3A10.0Z — Haemolytic anaemias due to hexose monophosphate shunt or glutathione metabolism anomalies, unspecified