ICD-11 classes
03 Diseases of the blood or blood-forming organs
Anaemias or other erythrocyte disorders
3A50 — Thalassaemias
3A50.0 — Alpha thalassaemia
3A50.02 — Haemoglobin H disease (– α/– – included)
ICD-11 3A50.02 — Haemoglobin H disease (– α/– – included)
Haemoglobin H (HbH) disease is a moderate to severe form of alpha-thalassemia characterised by pronounced microcytic hypochromic haemolytic anaemia.
The diagnosis includes nothing.
The diagnosis excludes nothing.
It has no clarifying diagnoses.