ICD-11 classes
03 Diseases of the blood or blood-forming organs
Anaemias or other erythrocyte disorders
3A50 — Thalassaemias
3A50.1 — Alpha thalassaemia related syndromes

ICD-11 3A50.1 — Alpha thalassaemia related syndromes

Alpha-thalassemia-related diseases refers to a group of diseases characterised by alpha-thalassemia and an associated disorder. Three conditions are included in this group: alpha-thalassemia-intellectual deficit syndrome, X-linked (or ATR-X syndrome), alpha-thalassemia-intellectual deficit syndrome and alpha-thalassemia-myelodysplastic disease or ATMDS.

The diagnosis includes nothing.

The diagnosis excludes nothing.

It has no clarifying diagnoses.