ICD-11 classes
03 Diseases of the blood or blood-forming organs
Anaemias or other erythrocyte disorders
3A51 — Sickle cell disorders or other haemoglobinopathies
3A51.6 — Haemoglobin D disease

ICD-11 3A51.6 — Haemoglobin D disease

Haemoglobin D (Hb D) disease is characterised by mild haemolytic anaemia and mild to moderate splenomegaly. Prevalence is unknown. Heterozygous forms of Hb D are clinically silent. Molecular testing can be useful to distinguish Hb D homozygosity from cases of heterozygous Hb D in association with beta-(0) thalassaemia.

The diagnosis includes nothing.

The diagnosis excludes nothing.

It has no clarifying diagnoses.