ICD-11 classes
03 Diseases of the blood or blood-forming organs
Anaemias or other erythrocyte disorders
3A70 — Aplastic anaemia
3A70.1 — Acquired aplastic anaemias
3A21.0 — Paroxysmal nocturnal haemoglobinuria
ICD-11 3A21.0 — Paroxysmal nocturnal haemoglobinuria
Paroxysmal nocturnal hemoglobinuria (PNH) is an acquired clonal hematopoietic stem cell disorder characterised by corpuscular haemolytic anaemia, bone marrow failure and frequent thrombotic events.
The diagnosis includes nothing.
It excludes 2 items.
- haemoglobinuria NOS (MF94)
- Aplastic anaemia with paroxysmal nocturnal haemoglobulinuria (3A70.1)
It has no clarifying diagnoses.
The diagnosis is coded elsewhere: