ICD-11 classes
03 Diseases of the blood or blood-forming organs
Anaemias or other erythrocyte disorders
3A72 — Sideroblastic anaemia

ICD-11 3A72 — Sideroblastic anaemia

Sideroblastic anaemias are a group of disorders in which haemoglobin is insufficiently synthesized, because of defective use of iron (although plasmatic iron levels may be normal or elevated). They are said to be sideroblastic because of the presence of ringed sideroblasts in the blood due to accumulated ferritin in mitochondria. Anaemias may be microcytic hypochrome (in thalassemia and hereditary sideroblastic anaemias), or macrocytic (in idiopathic acquired sideroblastic anaemias).

The diagnosis includes nothing.

The diagnosis excludes nothing.

Diagnosis with code 3A72 contains 3 clarifying diagnoses:

  1. 3A72.0 — Congenital sideroblastic anaemias
    It contains 4 clarifying diagnoses.
  2. 3A72.1 — Acquired sideroblastic anaemias
    It contains 1 clarifying diagnosis.
  3. 3A72.Z — Sideroblastic anaemia, unspecified

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