ICD-11 classes
03 Diseases of the blood or blood-forming organs
Coagulation defects, purpura or other haemorrhagic or...
3B62 — Qualitative platelet defects
3B62.0 — Inherited qualitative platelet defects

ICD-11 3B62.0 — Inherited qualitative platelet defects

A disease caused by genetically inherited mutations leading to abnormalities in platelets. This disease is characterised by abnormal platelet formation or function. Confirmation is by identification of mutations by genetic testing.

The diagnosis includes nothing.

The diagnosis excludes nothing.

Diagnosis with code 3B62.0 contains 6 clarifying diagnoses:

  1. 3B62.00 — Alpha-granule diseases
  2. 3B62.01 — Inherited giant platelet disorder
  3. 3B62.3 — Dense granule disease
  4. 3B62.4 — Alpha-delta dense granule deficiency
  5. 3B62.0Y — Other specified inherited qualitative platelet defects
  6. 3B62.0Z — Inherited qualitative platelet defects, unspecified

The diagnosis is included in 2 other classes.

  • Dense granule disease (3B62.3)
  • Alpha-delta dense granule deficiency (3B62.4)

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