ICD-11 classes
03 Diseases of the blood or blood-forming organs
Diseases of spleen
3B80 — Congenital disorders of spleen
3B80.0 — Splenomegaly in storage diseases

ICD-11 3B80.0 — Splenomegaly in storage diseases

A disease caused by storage diseases; genetically inherited metabolic disorders that result from defects in lysosomal, lipid or glycogen function, of the spleen. This disease is characterised by enlargement of the spleen. This disease may present with abdominal pain, chest pain, pallor, shortness of breath fatigue. Confirmation is through medical imaging.

The diagnosis includes nothing.

The diagnosis excludes nothing.

It has no clarifying diagnoses.