ICD-11 classes
04 Diseases of the immune system
Primary immunodeficiencies
4A01 — Primary immunodeficiencies due to disorders of adaptive...
4A01.2 — Diseases of immune dysregulation

ICD-11 4A01.2 — Diseases of immune dysregulation

The diagnosis has no description.

The diagnosis includes nothing.

The diagnosis excludes nothing.

Diagnosis with code 4A01.2 contains 6 clarifying diagnoses:

1. 4A01.20 — Immune dysregulation syndromes with hypopigmentation
2. 4A01.21 — Immune dysregulation syndromes presenting primarily with autoimmunity
3. 4A01.22 — Immune dysregulation syndromes presenting primarily with lymphoproliferation
4. 4A01.23 — Primary haemophagocytic lymphohistiocytosis
5. 4A01.2Y — Other specified diseases of immune dysregulation
6. 4A01.2Z — Diseases of immune dysregulation, unspecified

The diagnosis is coded elsewhere:

• Immune system disorders involving white cell lineages #3963
• Diseases of immune dysregulation #4032