ICD-11 classes
04 Diseases of the immune system
Nonorgan specific systemic autoimmune disorders
4A41 — Idiopathic inflammatory myopathy
4A41.0 — Dermatomyositis
4A41.01 — Juvenile dermatomyositis

ICD-11 4A41.01 — Juvenile dermatomyositis

Juvenile dermatomyositis is the early-onset form of dermatomyositis, a systemic autoimmune inflammatory muscle disorder, characterised by proximal muscle weakness, evocative skin lesion, and systemic manifestations.

The diagnosis includes nothing.

The diagnosis excludes nothing.

It has no clarifying diagnoses.

The diagnosis is coded elsewhere:

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