ICD-11 classes
04 Diseases of the immune system
Nonorgan specific systemic autoimmune disorders
4A44 — Vasculitis
4A44.1 — Aortic arch syndrome

ICD-11 4A44.1 — Aortic arch syndrome

Arteritis, often granulomatous, predominantly affecting the aorta and/or its major branches. Onset usually in patients younger than 50.

The diagnosis includes nothing.

The diagnosis excludes nothing.

It has no clarifying diagnoses.

The diagnosis is coded elsewhere:

• Vasculitis #18397