ICD-11 classes
04 Diseases of the immune system
Nonorgan specific systemic autoimmune disorders
4A44 — Vasculitis
4A44.9 — Immune complex small vessel vasculitis
4A44.92 — IgA vasculitis
ICD-11 4A44.92 — IgA vasculitis
Vasculitis, with IgA1-dominant immune deposits, affecting small vessels (predominantly capillaries, venules, or arterioles). Often involves skin and gut, and frequently causes arthritis. Glomerulonephritis indistinguishable from IgA nephropathy may occur.
It includes 1 item.
- Henoch-Schönlein purpura
The diagnosis excludes nothing.
It has no clarifying diagnoses.
The diagnosis is coded elsewhere:
- Vasculitis affecting small cutaneous blood vessels #16609
- Immune complex small vessel vasculitis #18407
The diagnosis is included in 2 other classes.
- Respiratory disorders in IgA vasculitis (CB05.4Y)
- Noninfectious enteritis or ulcer due to IgA vasculitis (DA94.Y)