ICD-11 classes
04 Diseases of the immune system
Nonorgan specific systemic autoimmune disorders
4A44 — Vasculitis
4A44.A — Antineutrophil cytoplasmic antibody-associated vasculitis
ICD-11 4A44.A — Antineutrophil cytoplasmic antibody-associated vasculitis
Necrotizing vasculitis, with few or no immune deposits, predominantly affecting small vessels (i.e., capillaries, venules, arterioles and small arteries), associated with MPO-ANCA or PR3-ANCA. Not all patients have ANCA. Add a prefix indicating ANCA reactivity, e.g. PR3-ANCA, MPO-ANCA, ANCA-negative.
The diagnosis includes nothing.
The diagnosis excludes nothing.
Diagnosis with code 4A44.A contains 5 clarifying diagnoses:
- 4A44.A0 — Microscopic polyangiitis
- 4A44.A1 — Granulomatosis with polyangiitis
- 4A44.A2 — Eosinophilic granulomatosis with polyangiitis
- 4A44.AY — Other specified antineutrophil cytoplasmic antibody-associated vasculitis
- 4A44.AZ — Antineutrophil cytoplasmic antibody-associated vasculitis, unspecified
The diagnosis is coded elsewhere: