ICD-11 classes
04 Diseases of the immune system
Nonorgan specific systemic autoimmune disorders
4A44 — Vasculitis
4A62 — Behçet disease
ICD-11 4A62 — Behçet disease
Behçet disease is a disease of incompletely understood aetiopathogenesis characterised by recurrent oral and/or genital aphthous ulcers accompanied by cutaneous, ocular, articular, gastrointestinal, and/or central nervous system inflammatory lesions. Small vessel vasculitis, thrombotic vasculopathy, arteritis and arterial aneurysms may occur. It has a high prevalence from the Eastern Mediterranean across Central Asia to China and Japan.
It includes 1 item.
- Adamantiades-Behçet disease
The diagnosis excludes nothing.
It has no clarifying diagnoses.
The diagnosis is coded elsewhere:
- Autoinflammatory disorders #3714
- Neutrophilic dermatoses #15772
- Autoinflammatory disorders #15863
- Vasculitis #18397
The diagnosis is included in 1 another class.
- Transient neonatal Behçet disease (KA07.Y)