ICD-11 classes
05 Endocrine, nutritional or metabolic diseases
Endocrine diseases
Disorders of the parathyroids or parathyroid hormone system
5A50 — Hypoparathyroidism
5A50.1 — Pseudohypoparathyroidism

ICD-11 5A50.1 — Pseudohypoparathyroidism

Pseudohypoparathyroidism is a condition with refractoriness to parathyroid hormone of its target tissues especially kidney that causes hypocalcaemia and hyperphosphataemia even in the presence of high circulating levels of biologically active parathyroid hormone.

The diagnosis includes nothing.

The diagnosis excludes nothing.

It has no clarifying diagnoses.

The diagnosis is coded elsewhere:

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