ICD-11 classes
05 Endocrine, nutritional or metabolic diseases
Endocrine diseases
Disorders of the gonadal hormone system
5A81 — Testicular dysfunction or testosterone-related disorders
LD2A.4 — 46,XY disorder of sex development due to androgen resistance
ICD-11 LD2A.4 — 46,XY disorder of sex development due to androgen resistance
Androgen insensitivity syndrome (AIS) is a disorder of sex development (DSD) characterised by the presence of female external genitalia, ambiguous genitalia or variable defects in virilization in a 46,XY individual with absent or partial responsiveness to age-appropriate levels of androgens. It comprises two clinical subgroups: complete AIS (CAIS) and partial AIS (PAIS).
The diagnosis includes nothing.
The diagnosis excludes nothing.
It has no clarifying diagnoses.
The diagnosis is coded elsewhere: