ICD-11 classes
05 Endocrine, nutritional or metabolic diseases
Endocrine diseases
Polyglandular dysfunction
5B00 — Autoimmune polyendocrinopathy

ICD-11 5B00 — Autoimmune polyendocrinopathy

This a subtype of autoimmune polyendocrine syndrome, in which multiple endocrine glands dysfunction as a result of autoimmunity. It is a genetic disorder attributed to a defect in the AIRE gene that normally confers immune tolerance. It is inherited in a recessive fashion.

The diagnosis includes nothing.

The diagnosis excludes nothing.

It has no clarifying diagnoses.