ICD-11 classes
05 Endocrine, nutritional or metabolic diseases
Metabolic disorders
Inborn errors of metabolism
5C50 — Inborn errors of amino acid or other organic acid metabolism
5C50.2 — Disorders of histidine metabolism

ICD-11 5C50.2 — Disorders of histidine metabolism

The diagnosis has no description.

The diagnosis includes nothing.

The diagnosis excludes nothing.

Diagnosis with code 5C50.2 contains 4 clarifying diagnoses:

  1. 5C50.20 — Histidinaemia
  2. 5C50.21 — Urocanic aciduria
  3. 5C50.2Y — Other specified disorders of histidine metabolism
  4. 5C50.2Z — Disorders of histidine metabolism, unspecified

The diagnosis is included in 1 another class.

  • Formiminoglutamic aciduria (3A02.Y)

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