ICD-11 classes
05 Endocrine, nutritional or metabolic diseases
Metabolic disorders
Inborn errors of metabolism
5C50 — Inborn errors of amino acid or other organic acid metabolism
5C50.4 — Disorders of lysine or hydroxylysine metabolism

ICD-11 5C50.4 — Disorders of lysine or hydroxylysine metabolism

The diagnosis has no description.

The diagnosis includes nothing.

It excludes 3 items.

  • Refsum disease (5C57.1)
  • Zellweger syndrome (5C57.0)
  • Glutaryl-CoA dehydrogenase deficiency (5C50.E1)

It has no clarifying diagnoses.

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