ICD-11 classes
05 Endocrine, nutritional or metabolic diseases
Metabolic disorders
Inborn errors of metabolism
5C50 — Inborn errors of amino acid or other organic acid metabolism
5C50.A — Disorders of urea cycle metabolism
ICD-11 5C50.A — Disorders of urea cycle metabolism
The diagnosis has no description.
The diagnosis includes nothing.
It excludes 2 items.
- Disorders of ornithine metabolism (5C50.9)
- Lysinuric protein intolerance (5C60)
Diagnosis with code 5C50.A contains 6 clarifying diagnoses:
- 5C50.A0 — Argininosuccinic aciduria
- 5C50.A1 — Carbamoylphosphate synthetase deficiency
- 5C50.A2 — Argininaemia
- 5C50.A3 — Citrullinaemia
- 5C50.AY — Other specified disorders of urea cycle metabolism
- 5C50.AZ — Disorders of urea cycle metabolism, unspecified