ICD-11 classes
05 Endocrine, nutritional or metabolic diseases
Metabolic disorders
Inborn errors of metabolism
5C50 — Inborn errors of amino acid or other organic acid metabolism
5C50.G — Trimethylaminuria

ICD-11 5C50.G — Trimethylaminuria

Trimethylaminuria is a metabolic disorder characterised by a body malodour similar to that of decaying fish.

It includes 1 item.

  • Fish odour syndrome

The diagnosis excludes nothing.

It has no clarifying diagnoses.

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