ICD-11 classes
05 Endocrine, nutritional or metabolic diseases
Metabolic disorders
Inborn errors of metabolism
5C58 — Inborn errors of porphyrin or heme metabolism

ICD-11 5C58 — Inborn errors of porphyrin or heme metabolism

The diagnosis has no description.

It includes 1 item.

  • defects of catalase and peroxidase

The diagnosis excludes nothing.

Diagnosis with code 5C58 contains 4 clarifying diagnoses:

  1. 5C58.0 — Disorders of bilirubin metabolism or excretion
    It contains 8 clarifying diagnoses.
  2. 5C58.1 — Porphyrias
    It contains 5 clarifying diagnoses.
  3. 5C58.Y — Other specified inborn errors of porphyrin or heme metabolism
  4. 5C58.Z — Inborn errors of porphyrin or heme metabolism, unspecified

The diagnosis is included in 1 another class.

  • X-linked sideroblastic anaemia, pyridoxine-responsive (3A72.00)

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