ICD-11 classes
05 Endocrine, nutritional or metabolic diseases
Metabolic disorders
Disorders of metabolite absorption or transport
5C63 — Disorders of vitamin or non-protein cofactor absorption or...
5C63.0 — Disorders of cobalamin metabolism or transport
3A01.0 — Hereditary Vitamin B12 deficiency anaemia

ICD-11 3A01.0 — Hereditary Vitamin B12 deficiency anaemia

This is a hereditary low blood level of vitamin B12. It can cause permanent damage to nervous tissue if left untreated long enough. Vitamin B12 itself was discovered through investigation of pernicious anaemia, which is an autoimmune disease that destroys parietal cells in the stomach that secrete intrinsic factor.

The diagnosis includes nothing.

The diagnosis excludes nothing.

It has no clarifying diagnoses.

The diagnosis is coded elsewhere:

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