ICD-11 classes
05 Endocrine, nutritional or metabolic diseases
Metabolic disorders
Disorders of metabolite absorption or transport
5C63 — Disorders of vitamin or non-protein cofactor absorption or...
5C63.2 — Disorders of vitamin D metabolism or transport
5C63.20 — Hypocalcaemic vitamin D dependent rickets

ICD-11 5C63.20 — Hypocalcaemic vitamin D dependent rickets

Hypocalcaemic vitamin D-dependent rickets (VDDR-I) is an early-onset hereditary vitamin D metabolism disorder characterised by severe hypocalcaemia leading to osteomalacia and rachitic bone deformations, and moderate hypophosphatemia.

The diagnosis includes nothing.

The diagnosis excludes nothing.

It has no clarifying diagnoses.

The diagnosis is coded elsewhere:

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