ICD-11 classes
08 Diseases of the nervous system
Movement disorders
8A01 — Choreiform disorders
8A01.0 — Benign hereditary chorea

ICD-11 8A01.0 — Benign hereditary chorea

Benign hereditary chorea should be considered in people with a relatively stable, nonprogressive chorea, in whom childhood onset and an autosomal dominant family history are present. Benign hereditary chorea can be associated with short stature and developmental delay. Larger deletions of causative gene, TITF-1, can cause a multisystem disorder with congenital hypothyroidism, hypotonia, and pulmonary problems.

The diagnosis includes nothing.

The diagnosis excludes nothing.

It has no clarifying diagnoses.