ICD-11 classes
08 Diseases of the nervous system
Movement disorders
8A02 — Dystonic disorders
8A02.0 — Primary dystonia

ICD-11 8A02.0 — Primary dystonia

Primary Dystonia (Primary Torsion dystonia) are disorders where dystonia is the sole neurological manifestation. These disorders are slowly progressive and are of which may be familial-genetic or sporadic.

The diagnosis includes nothing.

The diagnosis excludes nothing.

Diagnosis with code 8A02.0 contains 3 clarifying diagnoses:

  1. 8A02.00 — Benign essential blepharospasm
  2. 8A02.0Y — Other specified primary dystonia
  3. 8A02.0Z — Primary dystonia, unspecified

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