ICD-11 classes
08 Diseases of the nervous system
Movement disorders
8A03 — Ataxic disorders
8A03.1 — Hereditary ataxia

ICD-11 8A03.1 — Hereditary ataxia

A group of genetic disorders characterised by slowly progressive incoordination of gait and often associated with poor coordination of hands, speech, and eye movements

The diagnosis includes nothing.

Diagnosis with code 8A03.1 contains 9 clarifying diagnoses:

1. 8A03.10 — Friedreich ataxia
2. 8A03.11 — Ataxia due to Cerebrotendinous xanthomatosis
3. 8A03.12 — Ataxia due to Refsum disease
4. 8A03.13 — Ataxia due to abetalipoproteinemia
5. 8A03.14 — Hereditary episodic ataxia
6. 8A03.15 — Ataxia due to mitochondrial mutations
7. 8A03.16 — Spinocerebellar ataxia
8. 8A03.1Y — Other specified hereditary ataxia
9. 8A03.1Z — Hereditary ataxia, unspecified