ICD-11 classes
08 Diseases of the nervous system
Movement disorders
8A06 — Myoclonic disorders
8A06.0 — Essential myoclonus

ICD-11 8A06.0 — Essential myoclonus

This is a hereditary form of myoclonus, which is not usually associated with epilepsy or any other medical condition. Essential myoclonus tends to be stable without increasing in severity over time. More recently, it is believed that essential myoclonus may be the same as myoclonus-dystonia caused by a mutation in the sarcoglycan gene.

The diagnosis includes nothing.

The diagnosis excludes nothing.

It has no clarifying diagnoses.