ICD-11 classes
01 Certain infectious or parasitic diseases
Non-viral and unspecified infections of the central nervous...
1D01 — Infectious meningitis not elsewhere classified
1D01.0 — Bacterial meningitis
8E41 — Pachymeningitis

ICD-11 8E41 — Pachymeningitis

Inflammation of the pachymeninges resulting in localised or diffuse thickening of the dura mater which can be caused by chronic infection, inflammatory and immune-mediated disorders and malignancies. The cranial and/or the spinal dura may be affected. Neurological features includes headache, visual disturbance, cranial nerve palsies, ataxia and with spinal involvement, limb weakness, sensory impairment and sphincter disturbances . Diagnosis may be aided by neuroimaging and spinal fluid analysis.

The diagnosis includes nothing.

The diagnosis excludes nothing.

Diagnosis with code 8E41 contains 4 clarifying diagnoses:

  1. 8E41.0 — Pachymeningitis due to infection
  2. 8E41.1 — Idiopathic hypertrophic pachymeningitis
  3. 8E41.Y — Other specified pachymeningitis
  4. 8E41.Z — Pachymeningitis, unspecified

The diagnosis is coded elsewhere:

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