ICD-11 classes
08 Diseases of the nervous system
Disorders with neurocognitive impairment as a major feature
8A21 — Progressive focal atrophies
8A21.0 — Posterior cortical atrophy

ICD-11 8A21.0 — Posterior cortical atrophy

Benson's syndrome or Posterior Cortical Atrophy (PCA) refers to a clinical syndrome in which higher order visual processing is disrupted owing to a neurodegenerative disorder. The patients present with progressive and severe visual agnosia (inability to recognize and identify familiar objects or persons) and apraxia (loss in the ability to execute or perform skilled familiar movements).

The diagnosis includes nothing.

The diagnosis excludes nothing.

It has no clarifying diagnoses.